Iranian Journal of Pediatrics

Published by: Kowsar

Systemic Vasculitis and High IgE Level in a Patient with LPS-Responsive Beige-Like Anchor (LRBA) Deficiency

Jing Wu 1 , 2 , Wei-Fan Wang 1 , Tong-Xin Chen 1 , 2 , ** and Ji Chen 3 , *
Authors Information
1 Department of Allergy and Immunology, Shanghai Children’s Medical Center, School of Medicine, Shanghai Jiao Tong University, Shanghai, China
2 Division of Immunology, Institute of Pediatric Translational Medicine, Shanghai Children’s Medical Center, School of Medicine, Shanghai Jiao Tong University, Shanghai, China
3 Department of Dermatology, Shanghai Children’s Medical Center, School of Medicine, Shanghai Jiao Tong University, Shanghai, China
Corresponding Authors:
Article information
  • Iranian Journal of Pediatrics: 29 (2); e84691
  • Published Online: April 22, 2019
  • Article Type: Research Article
  • Received: September 28, 2018
  • Revised: January 16, 2019
  • Accepted: February 16, 2019
  • DOI: 10.5812/ijp.84691

To Cite: Wu J, Wang W, Chen T, Chen J. Systemic Vasculitis and High IgE Level in a Patient with LPS-Responsive Beige-Like Anchor (LRBA) Deficiency, Iran J Pediatr. Online ahead of Print ; 29(2):e84691. doi: 10.5812/ijp.84691.

Copyright © 2019, Author(s). This is an open-access article distributed under the terms of the Creative Commons Attribution-NonCommercial 4.0 International License ( which permits copy and redistribute the material just in noncommercial usages, provided the original work is properly cited.
1. Background
2. Objectives
3. Methods
4. Results
5. Discussion
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