Whole Lung Lavage of Nine Children with Pulmonary Alveolar Proteinosis: Experience in a Tertiary Lung Center

AUTHORS

Badiozaman Radpay 1 , Tahereh Parsa 2 , Shideh Dabir 3 , * , Mohammadreza Boloursaz 4 , Ahmadreza Arbab 5 , Seyyedahmad Tabatabaei 6

1

2

3

4

5

6

How to Cite: Radpay B, Parsa T, Dabir S, Boloursaz M, Arbab A, et al. Whole Lung Lavage of Nine Children with Pulmonary Alveolar Proteinosis: Experience in a Tertiary Lung Center, Iran J Pediatr. 2013 ; 23(1):95-99.

ARTICLE INFORMATION

Iranian Journal of Pediatrics: 23 (1); 95-99
Published Online: December 13, 2012
Article Type: Case Report
Received: March 03, 2011
Accepted: February 22, 2012

Crossmark

CHEKING

READ FULL TEXT
Abstract

Background: Pulmonary alveolar proteinosis (PAP) is a rare disease in children, characterized by intra-alveolar accumulation of large amounts of surfactant proteins, which severely reduce gas exchange. Whole lung lavage (WLL) is the preferred technique for the treatment of severe PAP.
Case Presentation: This report presents nine pediatric cases with advanced PAP who underwent WLL under general anesthesia during a 9 year period. One patient was treated with multiple unilateral WLL without employing cardiopulmonary bypass (CPB) and eight cases were treated by simultaneous lavage of both lungs using partial CPB.
Conclusion: Our experience suggested that partial CPB was useful to support oxygenation during WLL in small children with severe PAP in whom lung separation and selective lavaging of each lung were impracticable.

 

Keywords

Pulmonary Alveolar Proteinosis Children Cardiopulmonary Bypass Whole Lung Lavage

© 0, Author(s). This is an open-access article distributed under the terms of the Creative Commons Attribution-NonCommercial 4.0 International License (http://creativecommons.org/licenses/by-nc/4.0/) which permits copy and redistribute the material just in noncommercial usages, provided the original work is properly cited.

Fulltext

References

  • 1.

    References are available on the PDF.

  • COMMENTS

    LEAVE A COMMENT HERE: